{"product_id":"vrozhdennaq-nejtropeniq-von-amina-bouatai-und-sarra-berriri","title":"Vrozhdennaq nejtropeniq","description":"\u003cp\u003eVrozhdennaq nejtropeniq - äto gruppa redkih zabolewanij. Oni sootwetstwuüt deficitu kolichestwa nejtrofilow geneticheskogo proishozhdeniq i predstawlqüt soboj ochen' geterogennuü gruppu na fenotipicheskom i genotipicheskom urowne. Ona wstrechaetsq w dwuh formah: perwichnaq konstitucional'naq nejtropeniq i nejtropeniq, swqzannaq s geneticheskim zabolewaniem. Diagnoz osnowywaetsq na klinicheskih i biologicheskih dannyh: semejnyj i lichnyj anamnez, recidiwiruüschie bakterial'nye ili gribkowye infekcii, stojkaq nejtropeniq i specificheskie proqwleniq na mielogramme. Poslednie dostizheniq w oblasti genetiki i molekulqrnoj biologii pozwolili opisat' okolo dwadcati genow, otwetstwennyh za äti zabolewaniq. Tqzhest' infekcij pri wrozhdennoj nejtropenii swqzana s glubinoj i prodolzhitel'nost'ü nejtropenii i geneticheskim proishozhdeniem, chto trebuet sootwetstwuüschego wedeniq, osnowannogo na antibiotikoterapii i wwedenii G-KSF. Transplantaciq gemopoäticheskih stwolowyh kletok ostaetsq edinstwennym metodom lecheniq.\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786205279281\"\u003e\u003ch3\u003e\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786205279281","offer_id":40632216748125,"sku":"9786205279281","price":19.8,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/58d57f52-1394-42d2-a921-ad53d0cd99df.jpg?v=1758861988","url":"https:\/\/shop.autorenwelt.de\/products\/vrozhdennaq-nejtropeniq-von-amina-bouatai-und-sarra-berriri","provider":"Autorenwelt Shop","version":"1.0","type":"link"}