{"product_id":"semejnaq-sredizemnomorskaq-lihoradka-klinicheskij-obzor-von-hala-jel-basuni","title":"Semejnaq sredizemnomorskaq lihoradka: Klinicheskij obzor","description":"\u003cp\u003eSemejnaq sredizemnomorskaq lihoradka (FMF) (OMIM: 249100) - äto autosomno-recessiwnoe autowospalitel'noe geneticheskoe zabolewanie, swqzannoe s missens- i nonsens-mutaciqmi w gene MEFV, kotoryj raspolozhen na korotkom pleche hromosomy 16. Ono \"obychno woznikaet u lüdej sredizemnomorskogo proishozhdeniq, wklüchaq ewreew-sefardow, ewreew-mizrahi, armqn, azerbajdzhancew, arabow, grekow, turok i ital'qncew, hotq wse ätnicheskie gruppy wospriimchiwy k FMF, o chem soobschalos' w SShA i Yaponii. Harakternymi priznakami FMF qwlqütsq powtorqüschiesq äpizody peritonita, plewrita i artrita, obychno s soputstwuüschej lihoradkoj. Amiloidoz (anomal'noe otlozhenie osobogo belka, nazywaemogo amiloidom, w razlichnyh tkanqh organizma) qwlqetsq potencial'no ser'eznym oslozhneniem i mozhet razwiwat'sq bez qwnyh pristupow FMF. Pochki qwlqütsq osnownoj mishen'ü dlq amiloida. V nekotoryh sluchaqh neizwestno, pochemu nachinaütsq wspyshki FMF, no w kachestwe rasprostranennyh triggerow byli opredeleny sleduüschie: stress, holod, infekcii, nekotorye lekarstwa i menstrual'nyj cikl. Kolhicin chrezwychajno äffektiwen dlq predotwrascheniq pristupow FMF i preduprezhdeniq razwitiq amiloidoza.\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786205768884\"\u003e\u003ch3\u003e\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786205768884","offer_id":46354553930053,"sku":"9786205768884","price":19.8,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/e137f495-bb7a-4137-869b-417d82f8ff9d.jpg?v=1758516101","url":"https:\/\/shop.autorenwelt.de\/products\/semejnaq-sredizemnomorskaq-lihoradka-klinicheskij-obzor-von-hala-jel-basuni","provider":"Autorenwelt Shop","version":"1.0","type":"link"}