{"product_id":"poliglobuliniq-vakez-von-amina-bouatay-nesrine-ben-sayed-und-saoussen-dardour","title":"Poliglobuliniq Vakez","description":"\u003cp\u003ePolicitemiq Vakesa (PV) - äto mieloproliferatiwnoe nowoobrazowanie, woznikaüschee w rezul'tate klonal'noj äxpansii plüripotentnoj gemopoäticheskoj stwolowoj kletki, chto priwodit k proliferacii mieloidnoj tkani preimuschestwenno äritrocitarnogo rqda. On harakterizuetsq uwelicheniem obschej massy äritrocitow i gemoglobina bez chrezmernoj stimulqcii äritropoätinom. Ego rasprostranennost' nizka (2-3 sluchaq na 100 000 zhitelej w god). Nachal'naq stadiq zabolewaniq chasto protekaet bessimptomno. U nekotoryh pacientow wozniknowenie tromboticheskogo sobytiq ili simptomow, swqzannyh s sindromom giperwqzkosti, priwodit k diagnozu PV.Otkrytie mutacii JAK2 V617F polnost'ü izmenilo diagnostiku PV i pozwolilo ne tol'ko luchshe ponqt' patofiziologicheskie mehanizmy, no i razrabotat' celewuü molekulqrnuü terapiü, swqzannuü s äffektiwnym molekulqrnym monitoringom.\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786205294765\"\u003e\u003ch3\u003eDiagnosticheskie kriterii i aktual'nye woprosy lecheniq\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786205294765","offer_id":40642786984029,"sku":"9786205294765","price":19.8,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/31d35985-8311-4be4-8d9d-7b4ce3e8f492.jpg?v=1759297923","url":"https:\/\/shop.autorenwelt.de\/products\/poliglobuliniq-vakez-von-amina-bouatay-nesrine-ben-sayed-und-saoussen-dardour","provider":"Autorenwelt Shop","version":"1.0","type":"link"}