{"product_id":"osobennosti-apilepsii-swqzannoj-s-sindromom-ajkardi-von-imen-chabchub","title":"Osobennosti äpilepsii, swqzannoj s sindromom Ajkardi","description":"\u003cp\u003eSindrom Ajkardi (SA), obychno associiruüschijsq s tqzheloj äpilepsiej, tqzheloj psihomotornoj zaderzhkoj, chastichnoj ili polnoj ageneziej mozolistogo tela (MK) i horioretinal'nymi anomaliqmi, qwlqetsq ochen' redkim zabolewaniem, kotoroe w rawnoj stepeni porazhaet wse ätnicheskie gruppy. Ego rasprostranennost' oceniwaetsq ot 1\/105000 do 1\/167000 w SShA i ot 1\/93000 do 1\/99000 w nekotoryh ewropejskih stranah. Tochnaq rasprostranennost' AS neizwestna, no, po ocenkam, ona sostawlqet ne menee 853 sluchaew w SShA i bolee 4000 wo wsem mire. Pripadki, swqzannye s AS, chasto bywaüt qwnymi i poqwlqütsq rano, obychno w perwom trimestre zhizni. Spazmy obychno nahodqtsq na perednem plane. Oni obychno asimmetrichny. Vozmozhny i drugie tipy äpilepticheskih pripadkow. V osnownom äto fokal'nye pripadki, kotorye takzhe nachinaütsq rano i chasto predshestwuüt poqwleniü spazmow. Na mezhkriticheskoj älektroäncefalogramme nablüdaetsq harakternyj wid asimmetrichnoj i asinhronnoj gipsaritmii. Jeto takzhe swqzano s otsutstwiem sonnogo weretena i poqwleniem \"supressiwnogo wspleska\".\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786204340364\"\u003e\u003ch3\u003eJepilepsiq, swqzannaq s sindromom Ajkardi\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786204340364","offer_id":39663244214365,"sku":"9786204340364","price":19.8,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/e1a63061-9e1d-4edc-8b70-a40881ce5c20.jpg?v=1758003779","url":"https:\/\/shop.autorenwelt.de\/products\/osobennosti-apilepsii-swqzannoj-s-sindromom-ajkardi-von-imen-chabchub","provider":"Autorenwelt Shop","version":"1.0","type":"link"}