{"product_id":"mielodisplasticheskie-sindromy-von-maha-charfi-ikram-dammak-und-murad-chaari","title":"Mielodisplasticheskie sindromy","description":"\u003cp\u003eMielodisplasticheskie sindromy (MDS) - äto geterogennaq gruppa zabolewanij, swqzannyh s anomal'nym krowetworeniem i harakterizuüschihsq wysokim riskom progressirowaniq w ostryj mieloidnyj lejkoz (OML). Cel' nashej raboty - opredelit' äpidemiologicheskie, klinicheskie, citologicheskie, prognosticheskie i terapewticheskie harakteristiki MDS na üge Tunisa. My wklüchili w issledowanie 41 pacienta s MDS. Sootnoshenie polow sostawilo 1,56. Srednij wozrast sostawil 63 goda. Osnownym klinicheskim proqwleniem pri postanowke diagnoza byl anemicheskij sindrom (86 %), priznaki displazii äritrocitow, granul i trombocitow byli wyqwleny w 68, 81 i 66 % mielogramm sootwetstwenno. MDS-EB2 byl dominiruüschim tipom MDS w nashej serii (38 %) soglasno klassifikacii VOZ 2016 goda. Kariotip byl anomal'nym w 62 % sluchaew. Naibolee chastymi hromosomnymi aberraciqmi byli slozhnyj kariotip i deleciq 5q. Samoj wysokoj gruppoj riska po shkale IPSS byla gruppa wysokogo riska (31 %). Specificheskoe lechenie bylo naznacheno w 30 % sluchaew. Obschaq wyzhiwaemost' (OV) w techenie odnogo goda sostawila 56 %.\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786207102068\"\u003e\u003ch3\u003eklinicheskie, biologicheskie, prognosticheskie i terapewticheskie aspekty\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786207102068","offer_id":47574921249093,"sku":"9786207102068","price":79.9,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/c83e10cc-a098-41bf-b2e2-dc1ec4becfa0.jpg?v=1747897095","url":"https:\/\/shop.autorenwelt.de\/products\/mielodisplasticheskie-sindromy-von-maha-charfi-ikram-dammak-und-murad-chaari","provider":"Autorenwelt Shop","version":"1.0","type":"link"}