{"product_id":"chelowek-s-boleznu-hantingtona-von-ugo-mojta-dos-santos-alexandra-dinis-und-magda-guerra","title":"Chelowek s bolezn'ü Hantingtona","description":"\u003cp\u003eV poslednie desqtiletiq bolezn' Hantingtona priwlekaet znachitel'noe wnimanie nauchnogo soobschestwa. Nesmotrq na äto, molekulqrnye mehanizmy, swqzannye s genezom ätogo rasstrojstwa, wse esche nedostatochno qsny. Izwestno, chto äto autosomno-dominantnoe zabolewanie s polnoj penetrantnost'ü, woznikaüschee pri nalichii specificheskogo gena na chetwertoj hromosome. Patologiq obychno harakterizuetsq pozdnim nachalom, a ee klinicheskie proqwleniq (dwigatel'nye narusheniq, psihicheskie rasstrojstwa i kognitiwnye narusheniq) rezko uhudshaüt kachestwo zhizni bol'nyh.Bylo oprobowano mnozhestwo terapewticheskih strategij, no slozhnost' mnogochislennyh mehanizmow, priwodqschih k nejrodegeneracii, nablüdaemoj pri ätom zabolewanii, sposobstwuüt otsutstwiü uspeha w poiske äffektiwnogo lecheniq. Jeto progressiruüschee zabolewanie, i do sih por ne suschestwuet specificheskogo lecheniq, no prawil'naq orientaciq cheloweka i ego sem'i na preimuschestwa prawil'nogo pitaniq, wypolnenie reabilitacionnyh uprazhnenij i farmakologicheskoe lechenie sposobstwuüt uluchsheniü kachestwa ih zhizni.\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786205226308\"\u003e\u003ch3\u003eFunkcional'naq i kognitiwnaq ocenka\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786205226308","offer_id":40634512212061,"sku":"9786205226308","price":19.8,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/86a52a1a-f77a-4bf4-9c24-222517313178.png?v=1758878824","url":"https:\/\/shop.autorenwelt.de\/products\/chelowek-s-boleznu-hantingtona-von-ugo-mojta-dos-santos-alexandra-dinis-und-magda-guerra","provider":"Autorenwelt Shop","version":"1.0","type":"link"}