{"product_id":"vsestoronnij-obzor-po-ihtiozu-von-sumajq-nahid","title":"Vsestoronnij obzor po ihtiozu","description":"\u003cp\u003eIhtioz - äto bol'shaq, klinicheski, geneticheski i ätiologicheski geterogennaq gruppa narushenij orogoweniq, obuslowlennyh anomal'noj differenciaciej i deskwamaciej äpidermisa. Hotq oni razlichaütsq po klinicheskim priznakam, nasledstwennosti, strukturnym i biohimicheskim anomaliqm äpidermisa, oni chasto predstawlqüt soboj diagnosticheskuü problemu. Jeti kozhnye zabolewaniq qwlqütsq rezul'tatom nalichiq chrezmernogo kolichestwa suhih powerhnostnyh cheshuek iz-za wyrazhennoj keratinizacii ili orogoweniq, kak sledstwie anomal'noj äpidermal'noj differenciacii i metabolizma. Na segodnqshnij den' oficial'no opisano pqt' osnownyh tipow IT, k kotorym otnosqtsq wul'garnyj ihtioz, lamellqrnyj ihtioz, äpidermoliticheskij giperkeratoz, wrozhdennaq ihtioziformnaq äritrodermiq i H-sceplennyj ihtioz. Ih mozhno differencirowat' na osnowanii obschih klinicheskih proqwlenij, gistologicheskih dannyh, a takzhe geneticheskogo materiala. Molekulqrnye dannye pokazywaüt funkcional'noe znachenie i wzaimodejstwie mnogih razlichnyh äpidermal'nyh belkow i metabolicheskih putej, wklüchaq osnownye strukturnye belki (keratiny, lorikrin), fermenty, uchastwuüschie w lipidnom obmene, peroxisomal'nom transporte i obrabotke, a takzhe reparacii DNK.\u003c\/p\u003e\u003cdiv class=\"aw-variant-hidden-subtitle-div\" id=\"aw-variant-subtitle-9786204939438\"\u003e\u003ch3\u003esemejstwo geneticheskih zabolewanij kozhi\u003c\/h3\u003e\u003c\/div\u003e","brand":"Autorenwelt Shop","offers":[{"title":"Softcover - 9786204939438","offer_id":40287112331357,"sku":"9786204939438","price":24.8,"currency_code":"EUR","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0940\/0622\/files\/6083071b-6954-4a5f-b1ba-5160164b80f3.jpg?v=1759300471","url":"https:\/\/shop.autorenwelt.de\/en\/products\/vsestoronnij-obzor-po-ihtiozu-von-sumajq-nahid","provider":"Autorenwelt Shop","version":"1.0","type":"link"}